Europace Advance Access published online on May 22, 2007
Europace, doi:10.1093/europace/eum077
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CASE REPORT
Catheter ablation of multiple, surgically created, atrioventricular connections following FontanBjörk procedure
1 Arrhythmia Unit, Department of Cardiology, Hospital Universitario La Paz, Universidad Autónoma, Paseo de la Castellana 261, 28046 Madrid, Spain; 2 Adult Congenital Heart Diseases Unit, Department of Cardiology, Hospital Universitario La Paz, Universidad Autónoma, Paseo de la Castellana 261, 28046 Madrid, Spain
An increased incidence of WolffParkinsonWhite (WPW) syndrome with tricuspid atresia has been reported. Although atrioventricular accessory pathways may develop across suture lines after the FontanBjörk procedure, the presence of multiple acquired accessory pathways has only been described rarely. We report on a case of a female with tricuspid atresia who underwent the Fontan operation at 5 years of age. One year later, she developed a WPW pattern. Narrow complex tachycardias started at the age of 18. An electrophysiological study revealed the presence of three accessory pathway connections at the surgical anastomosis level. All of them were successfully ablated and there were no recurrences.
Key Words: Tricuspid atresia, Fontan procedure, WolfParkinsonWhite syndrome, Catheter ablation
* Corresponding author. Tel: +34 91 7277564; fax: +34 91 7277564. E-mail address: rpeinado{at}secardiologia.es
Manuscript submitted 15 November 2006. Accepted after revision 2 April 2007.