© 2002 by European Society of Cardiology
CASE REPORT
Ebstein's anomaly, atrial paralysis and atrio-ventricular block: an uncommon association
Arrhythmia and Pacing Clinic, Cardiology Department, Instituto Nacional de Ciencias Médicas y Nutrición, ‘Salvador Zubirán’ México D.F.
We report here the case of a 22-year-old female patient with an incomplete Ebstein's anomaly, complete heart block and atrial standstill. Atrial paralysis associated with Ebstein's anomaly is the most important feature, since there is a report of familial Ebstein's anomaly associated with atrial standstill but isolated cases have not been described. The patient presented with atypical chest pain and a symptomatic bradycardia of 37 beats per minute. A VVIR pacemaker was implanted. She has subsequently been symptom free.
Key Words: Ebstein's anomaly, atrial standstill, complete atrio-ventricular block, VVIR pacemaker
Correspondence: Dr Enrique Asensio Lafuente, Dr Julio Carballal Sanjurjo, Clínica de Arritmias y Marcapasos, Departamento de Cardiología, Instituto Nacional de Ciencias Médicas y Nutrición, ‘Salvador Zubirán’, Vasco de Quiroga # 15, Col. Sección XVI, Tlalpan, México 14000 D.F., México. Tel.: (525) 573 1200; Fax: (525) 655 3306. e-mail: julitocorreo{at}hotmail.com; easensio{at}avantel.net
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