© 1999 by European Society of Cardiology
CASE REPORT
Rare association of hypertrophic cardiomyopathy and complete atrioventricular block with prompt disappearance of outflow gradient after DDD pacing
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NçkalDepartment of Cardiology, Izmir Ataturk State Hospital Izmir, Turkey
Although arrhythmias are common in hypertrophic cardiomyopathy (HCM), complete atrioventricular (AV) block is very unusual. A 27-year-old female presented with a recent history of syncope and exercise intolerance. ECG demonstrated complete AV block. Two-dimensional Doppler echocardiography revealed HCM with a 60 mmHg left ventricular outflow tract (LVOT) gradient. A temporary transvenous ventricular pacemaker was inserted urgently, and subsequently replaced by a permanent DDD pacemaker. All symptoms were eliminated. This symptomatic improvement was associated with complete disappearance of LVOT gradient at the time of implantation. No gradient was observed during early follow-up and at 6 months after DDD pacemaker implantation.
Key Words: Hypertrophic Obstructive cardiomyopathy, atrioventricular block, DDD pacemakers
Correspondence: Serdar Bayata, MD, 2040 Sokak, P:04 Blok, 58. Giris No:46, Bostanli, zmir, Turkey.
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